Congenital Hepatoportal Arteriovenous Fistula associated with Intrahepatic Portal Vein Aneurysm and Portohepatic Venous Shunt: Case Report

quired as a result of trauma, including a liver biopsy, or in association with hepatic tumors and ruptured aneurysms of the hepatic artery (1). A congenital hepatoportal arteriovenous fistula is extremely rare and there are very few reports. The common clinical manifestations are the features of portal hypertension such as bowel congestion, gastrointestinal bleeding, malabsorption, ascites and splenomegaly (2). An intrahepatic portovenous shunt is also rare (3). Duplex Doppler sonography is the modality of choice for both diagnosing and evaluating abnormal vascular communications along with their hemodynamic consequences in the liver, which can be confirmed by angiography (4). We describe a case of a male neonate who was diagnosed by duplex Doppler sonography with a congenital hepatoportal arteriovenous fistula and portohepatic venous shunt associated with an intrahepatic portal vein aneurysm, which was confirmed by angiography.